TY - JOUR
T1 - A spinal intradural enderogenous cyst with well-differentiated muscularis propria
AU - ten Donkelaar, H. J.
AU - Willemsem, M. A.A.P.
AU - van der Heijden, I.
AU - Beems, T.
AU - Wesseling, P.
PY - 2002
Y1 - 2002
N2 - We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to severe myelopathy led to the death of the child 19 days postpartum. At autopsy, a well-differentiated enterogenous cyst was found, the cyst wall containing gastric and esophageal type mucosa, and a bona fide muscularis propria. The gastrointestinal tract was completely normal. The possible developmental history of intradural enterogenous cysts is discussed.
AB - We report a case of a newborn presenting with severe compression of the spinal cord due to a large, solitary mass extending from C4 to T2. Neurosurgical exploration revealed a large intradural, extramedullary cystic lesion, compressing the spinal cord. Slowly progressive respiratory failure due to severe myelopathy led to the death of the child 19 days postpartum. At autopsy, a well-differentiated enterogenous cyst was found, the cyst wall containing gastric and esophageal type mucosa, and a bona fide muscularis propria. The gastrointestinal tract was completely normal. The possible developmental history of intradural enterogenous cysts is discussed.
KW - Enterogenous cyst
KW - Myelopathy
KW - Neurenteric cyst
KW - Spinal cord compression
KW - Split notochord syndrome
UR - http://www.scopus.com/inward/record.url?scp=0036831809&partnerID=8YFLogxK
U2 - 10.1007/s00401-002-0599-4
DO - 10.1007/s00401-002-0599-4
M3 - Article
C2 - 12410402
AN - SCOPUS:0036831809
SN - 0001-6322
VL - 104
SP - 538
EP - 542
JO - Acta Neuropathologica
JF - Acta Neuropathologica
IS - 5
ER -