Malignant ectomesenchymoma in children: The European pediatric Soft tissue sarcoma Study Group experience

Giuseppe Maria Milano, Daniel Orbach, Michela Casanova, Pablo Berlanga, Reineke A. Schoot, Nadege Corradini, Bernadette Brennan, Gema L. Ramirez-Villar, Lisa Lyngsie Hjalgrim, Max M. van Noesel, Rita Alaggio, Andrea Ferrari

Onderzoeksoutput: Bijdrage aan tijdschriftArtikelpeer review

Samenvatting

Malignant ectomesenchymoma (MEM) is an extremely rare soft tissue tumor typical of young children, currently included in the category of skeletal muscle malignancies and characterized by a neuroblastic component. This study describes a series of 10 patients prospectively registered in the European paediatric Soft tissue sarcoma Study Group (EpSSG) database Of the 10 cases, seven had an initial local diagnosis of rhabdomyosarcoma. All patients received chemotherapy according to rhabdomyosarcoma strategy, four had radiotherapy. Overall, six patients were alive in first remission, two in second remission and one after second tumor. Only the patient with initially metastatic tumor died of disease.

Originele taal-2Engels
TijdschriftPediatric Blood and Cancer
DOI's
StatusGeaccepteerd/In druk - 2022

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